Cerebellar meningeal melanocytoma associated with nevus of Ota: An extremely rare case.

A 20-year-old woman presented with a 2-day history of headache. She had a congenital grayish-blue pigmented nevus on her left side face, which involved ipsilateral sclera and oral mucosal membrane, diagnosed as nevus of Ota (figure 1, A and B). Neuroradiologic manifestation revealed a lesion in the left cerebellar hemisphere, the etiology of the presenting tumor apoplexy (figure 1, C–F). A left cerebellar hemisphere craniotomy was performed. A well-defined black lesion involved dura mater to the pia mater and was firmly attached to the cerebellar tentorium (figure 2, A and B). Histopathologic examination confirmed a meningeal melanocytoma. Postoperative CT demonstrated total tumor resection. Figure 1 Photograph of the patient and preoperative brain MRI and CT